Figure 2

Macroscopic and microscopic images. Upper left: Macroscopic appearance. The ectopic liver is attached on the right side of the gall bladder, in the fundus. Upper right: Histologic appearance. The portal veins are easily identified in their y-appearance. Next to them the draining common bile duct (HE, 40×). Lower left: PAS positive and D-PAS resistant intracellular globules (D-PAS, 600×) Lower right: Immunhistochemistry for alpha1-antitrypsin shows multiple positive intracellular droplets (alpha1-antitrypsin, 600×)