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Table 1 Diagnosis of the different IP subtypes in 3 steps

From: Diagnostic approach to interstitial pneumonias in a single centre: report on 88 cases

Interstitial lung diseases (n = 88)

Step 1: histology alone (pattern)

Step 2: histology + clinical information

Step 3: interdisciplinary case evaluation

Idiopathic interstitial pneumonia or pattern*

85

77

63

  IPF/Usual interstitial pneumonia (UIP)

31

29

27

  Non specific interstitial pneumonia (NSIP)

21

20

14

  Respiratory bronchiolitis with ILD (RBILD)

14

10

6

  Desquamative interstitial pneumonia (DIP)

3

3

3

  Cryptogenic organizing pneumonia (COP)

13

12

10

  Acute interstitial pneumonia (AIP)

1

1

0

  Lymphocytic interstitial pneumonia (LIP)

3

3

3

Non idiopathic interstitial pneumonia

3

11

25

  Hypersensitivity pneumonitis (HP)

0

3

10

  Langerhans cell histiocytosis (LCH)

3

7

7

  IP of other known causes or associations

0

1

8

Correctness of diagnosis (total)

67%*

87%*

100%

  1. *p < 0.05 vs interdisciplinary case evaluation (exact Fisher test).