Table 1 Reported Cases of PEComatosis in the English Language Literature (5 Cases)

Fadare 2004 [12]

41/F

Myometrium, small bowel lamina propria, ovarian hila/2.2

No cytological atypia, mitotic activity or necrosis.

HMB-45 positive

With TSC. No recurrence or metastases at 35 months' follow-up.

Salviato 2006 [13]

70/F

Diffuse peritoneum/6

Epithelioid and spindle cells, mild to moderate nuclear pleomorphism, focal areas of necrosis.

HMB45, melan-A, and SMA positive, desmin and S100 negative.

With a history of ancient hysterectomy for fibroids

Liang 2008 [14]

59/F

Pelvic lymph nodes, myometrium, cervix, and ovary/2.6

Marked nuclear pleomorphism, necrosis, 2 mitoses/50 HPF, occasional atypical mitosis, infiltrative borders.

HMB45, melan-A, SMA and ER positive.

With TSC.

Froio 2008 [15]

39/F

Uterine corpus, both ovaries, and the omentum/

HMB45, melan-A, SMA, ER and PR positive.

With TSC.

Lim 2011 [16]

59/F

Uterine, cervix, uterine corpus.

Mature adipose tissue, spindle cells, small nests of clear epithelioid cells

With TSC.