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Table 1 Vulvar proximal type epithelioid sarcoma: the current literature review

From: Vulvar “proximal-type” epithelioid sarcoma: report of a case and review of the literature

Author

Year

Age

Surgery

RT

CT

Recurrent site

DFS (months)

OS (months)

Piver SM et al.[4]

1972

1

27

Wide local excision

No

No

None

-

NED (108)

Gallup DG et al.[6]

1976

1

31

Radical vulvectomy

No

No

None

-

NED (16)

Hall DJ et al.[7]

1980

1

31

Wide local excision, inguinal lymph node dissection

No

No

Local, lymph node, lung

35

DOD (70)

Ulbright TM et al.[8]

1983

2

55

Local excision

No

No

Local, lung, abdominal wall, skin

8

DOD (15)

30

Wide local excision

No

Yes

Local, Lung

2

DOD (8)

Tan GWT et al.[9]

1989

1

21

Wide local excision

No

No

None

-

NED (36)

Perrone T et al.[10]

1989

1

21

Local excision, lymph node dissection

No

No

None

-

NED (56)

Wevers AC et al.[11]

1989

1

21

Local excision, lymph node dissection

No

No

Local recurrence

2

DOD (5)

Weissmann D et al.[12]

1990

1

26

Local excision

No

No

Local lymph node, lung, scalp, liver, kidney

14

AWD (78)

Hernandez-Ortiz MJ et al.[13]

1995

1

51

Radical vulvectomy

No

No

Lung

5

DOD (8)

Konefka T et al.[14]

1994

1

49

Radical vulvectomy and bilateral inguinal lymph node dissection

No

Yes

Lung

5

DOD (8)

Guillou L et al.[15]

1997

3

57

Local excision

Yes

No

None

-

DOID (52)

49

Radical vulvectomy

Yes

No

None

-

NED (22)

45

Wide local excision

No

Yes

None

-

NED (21)

Tjalma WA et al.[16]

1999

1

23

Hemivulvectomy

No

No

None

-

NED (48)

Kasamatsu T et al.[17]

2001

1

23

Local excision

No

No

Local lymph node

96

NED

 

2001

3

37

Local excision

No

Yes

None

-

NED (11)

30

Local excision

No

No

Local lymph node, skin

96

NED (104)

80

Wide local excision

No

No

Local lymph node, lung

16

DOD (23)

Altundag K et al.[5]

2004

1

51

Left hemivulvectomy with bilateral inguinal lymph node dissection

No

Yes

Lung

4

DOD (6)

Dainese E et al.[19]

2005

1

34

Right emivulvectomy with right inguinal lymph node dissection

No

No

None

-

NED (12)

Argenta PA et al.[20]

2007

1

35

Radical excision, inguinal-femoral lymph node dissection

Yes

No

None

-

NED (40)

Kim JH et al.[21]

2008

1

24

Clitoris sparing wide local excision

No

No

None

-

NED (8)

Rai H et al.[22]

2009

1

17

Local excision, lymph node dissection

Yes

No

Local lymphnode

2

AWD (2)

Tholpady A et al.[23]

2010

1

17

Radical excision

No

No

-

-

NED (12)

Chiyoda T et al.[24]

2011

1

33

Left radical vulvectomy

No

No

None

-

NED (36)

Andrisani A et al.[25]

2011

1

46

Radical superior vulvectomy

Yes

Yes

Local lymph nodes, abdominal wall, genital, inguinal and thigh muscles, bladder

1

DOD (11)

Kim HJ et al.[26]

2012

1

41

Local excision

No

No

None

-

NED (10)

Ong AC et al.[27]

2012

1

51

Right emivulvectomy and right inguinal lymph node dissection

No

No

None

-

NED (8)

Our study

 

1

63

Bilateral radical vulvectomy, right inguinal lymph node dissection

Yes

No

Inguinal lymph node

-

NED (14)

  1. NED no evidence of disease, DOD dead of disease, DOID dead of inter current disease, AWD alive with disease, RT radiotherapy, CT chemotherapy, DFS disease free survival, OS overall survival.