Malignant perivascular epithelioid cell tumor of mesentery with lymph node involvement: a case report and review of literature

Table 1 Clinicopathological features of mesenteric PEComas described in present and previous reports

No.	Authors (yr.)	Diagnosis	Age (year)/Gender	Tumor size (cm)	Nuclear grade	Cellularity	MF (per 50HPF)	Invasion	Necrosis	LN status	Treatment	Outcome
1	Folpe AL (2005) [3]	PEComa with UMP	67/Female	13.0	High	Moderate	0	No	No	Not involved	SE only	NED at 84 months
2		Benign PEComa	97/Female	4.0	Intermediate	Moderate	0	No	No	Not involved	SE only	NED at 38 months
3		Malignant PEComa	80/Female	9.5	High	High	>50	Vascular invasion	Yes	Not involved	SE only	NED at 19 months
4		Malignant PEComa	46/Female	12.0	Intermediate	Moderate	5	Vascular invasion	Yes	Not involved	SE + CT	Recur and liver metastases at 22 months; die at 27 months
5	Gross E (2010) [4]	Malignant PEComa	5.5/Male	5.0	High	Moderate	NA	Surrounding tissue invasion	No	Not involved	SE only	NED at 24 months
6	Lai CL (2012) [5]	Malignant PEComa	59/Male	11.0	High	High	3	Vascular invasion	Yes	Not involved	SE + CT	Recur at 6 months; alive
7	The present case	Malignant PEComa	38/Female	10.0	Intermediate	Moderate	2	Surrounding tissue invasion	Yes	Involved	SE + CT	NED at 6 months

UMP, uncertain malignant potential; MF, mitotic figure; LN, lymph node; SE, surgical excision; CT, chemotherapy; NA, not available; NED, no evidence of disease.

ISSN: 1746-1596