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Table 2 Clinical data

From: Epithelioid Hemangioendothelioma: clinicopathologic, immunhistochemical, and molecular genetic analysis of 39 cases

Case

Sex/Age

Site

Size (cm)

Therapy

Rec/Met, m

Follow-up

1

f/42y

toe

2.0

E

NA

NA

2

f/63y

occipital

1.0

WE, RT, ME

cerv LN, 14

NED, 2y

3

f/58y

groin

NA

NA

NA

NA

4

f/66y

lung (mf)

NA

NA

NA

NA

5

m/69y

oral cavity

0.8

WE

-

NED, 2y

6

m/42y

groin

3.6

NA

NA

NA

7

m/10y

nose bridge

1.1

NA

NA

NA

8

m/14y

LN, groin

2.0

WE

NA

NA

9

f/70y

heel

1.1

NA

NA

NA

10

m/61y

skin/finger

0.5

WE

-

NED, 2y

11

f/71y

neck

1.1

E, R1

-

NED, 7y

12

m/51y

thoracic spine

NA

NA

NA

NA

13

f/30y

upper arm

1.9

NA

NA

NA

14

m/70y

lower arm

2.0

NA

NA

NA

15

f/85y

paravertebral

5.4

NA

NA

NA

16

f/78y

breast

NA

NA

NA

NA

17

f/41y

neck

2.5

WE, RT

-

NED, 3m

18

f/60y

axilla

4.5

E, RT

-

NED, 1y

19

m/68y

lung

1.4

WE, TKI*

lung, pleura, mediastinum, 13

AWD, 2y

20

m/54y

lung

2.2

WE

NA

NA

21

m/43y

mediastinum

7.5

E

NA

NA

22

f/46y

liver (mf)

4.5

WE

-

NED, 1y

23

f/70y

liver

NA

CT

pleura, 0

AWD, 1.5y

24

m/49y

maxilla

3.1

WE, RT,ME

cerv LN, 5

NED, 1y

25

f/26y

humerus

NA

E

-

NED, 5y

26

m/10y

paratesticular

1.4

E

NA

NA

27

f/55y

rib

4.5

WE

NA

NA

28

f/49y

mandible

2.5

WE

cerv LN

NA

29

f/37y

neck

3.0

E

LN,bone,lung

DOD, 4 m

30

f/81y

femur

NA

NA

NA

NA

31

m/19y

lung (mf)

NA

NA

NA

NA

32

f/41y

groin

1.8

WE, RT

Vulva

NED, 1y

33

f/77y

pubic skin

2.5

WE

-

NED, 3y

34

m/59y

lung

3.0

WE, ME

pleura, bone, mesentery, 3

DOD, 1.5y

35

f/25y

neck

7.5

E

cerv LN, 0

NA

36

f/9y

lung (mf)

NA

CT

pleura

DOD, 0.5y

37

f/10y

lung (mf)

11

CT, RT

chest wall

DOD, 0.5y

38

m/51y

elbow

2.4

E

NA

NA

39

f/75y

neck

2.5

WE

NA

NA

  1. Rec, Recurrence; Met, Metastases; m, Months; y, Year(s); E, Excision; WE, Wide excision; mf, Multifocal; NED, No evidence of disease; AWD, Alive with disease; DOD, death of disease; RT, Radiotherapy; CT, Chemotherapy; ME, Metastasectomy; NA, Not available; cerv, Cervical; LN, Lymph node; int jug vein, internal jugular vein; TKI*, Tyrosine kinase inhibitor pazopanib.