Table 2 Summary of reported cases of primary renal SEF
Authors | Age (years) | Gender | Largest Diameter /Laterality | Clinical presentation | FISH Findings | Therapy | Metastases | Outcome (mo) |
|---|---|---|---|---|---|---|---|---|
Arbajian, et al. [1] | 41 | Female | 9 cm/NS | NS | EWSR1 Del 3′ | NS | Bone and lung | DOD (22) |
Argani, et al. [8] | 17 | Male | 25 cm/L | Left flank, back and abdominal pain, weight loss, dysuria, and decreased appetite | EWSR1-CREB3L1 fusion | Surgery + RT | Rib, vertebrae, epidural spinal cord and liver | DOC (1) |
Argani, et al. [8] | 61 | Female | 5 cm/L | Rib pain | EWSR1-CERB3L1 fusion | Surgery | Ribs, bone, lung and lymph nodes | AWD (6) |
Ohlmann, et al. [9] | 24 | Female | 22 cm/R | NS | No results | Surgery + RCT | Lungs and vertebrae | DOD (82) |
Ohlmann, et al. [9] | 43 | Male | 4.2 cm/R | Incidental | EWSR1 split | Surgery | None | ANED (8) |
Ertoy Baydar, et al. (present case) | 16 | Female | 7.5 cm/L | Abdominal pain radiating to back on the left | EWSR1-CREB3L1 fusion | Surgery + CT | Lungs, vertebrae, sacrum and left femoral head | AWD (30) |
Ertoy Baydar, et al. (present case) | 57 | Female | 7.5 cm/L | Incidental | EWSR1-CREB3L1 fusion | Surgery | None | ANED (10) |