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Table 1 Clinical features of 25 cases of epithelioid inflammatory myofibroblastic sarcoma

From: Epithelioid inflammatory myofibroblastic sarcoma: a clinicopathological, immunohistochemical and molecular cytogenetic analysis of five additional cases and review of the literature

Case

Age/Sex

Site

Size (cm)

Multifocal

Treatment

Recurrence

Metastasis

Follow up

Source

1

7y/M

Abdominal cavity

NA

No

SE, CT

Yes (5w, 5 m)

No

NED(5 m)

Ma et al. [7]

2

7 m/M

Mesentery and omentum

11

Yes

SE

Yes (8 m)

No

AWD(8 m)

 

3

2y/M

Retroperitoneal and abdominal cavity

10

No

SE

No

No

NED(36 m)

Patel et al. [6]

4

34y/M

Liver

8

No

SE

Yes (5 m)

No

DOD(5.5 m)

Chen et al. [8]

5

44y/M

Omentum

NA

Yes

SE, CT, ALKi

Yes (5 m)

Liver (12 m)

AWD(39 m)

Butrynski et al. [9]

6

41y/M

Omentum

26

Yes

ST, CT, ALKi

Yes (12 m)

Liver(12 m)

NED(40 m)

Marino-Enriquez et al. [4]

7

59y/M

Mesentery of small bowel

15

Yes

SE, CT

Yes

No

DOD (12 m)

 

8

6y/M

Omentum

10.5

No

SE, CT

Yes

No

AWD(3 m)

 

9

28y/M

Mesentery of small bowel

NA

Yes

NA

NA

NA

NA

 

10

63y/M

Mesentery of small bowel

25

No

SE, CT

Yes

No

DOD(3 m)

 

11

42y/M

Intra-abdominal

NA

No

SE, CT

Yes

No

AWD(13 m)

 

12

7 m/M

Peritoneum

10

No

SE, CT, RT

Yes

No

DOD(36 m)

 

13

40y/M

Peritoneum

8

No

SE, CT, RT

Yes

Lung, liver, and lymph node

  

14

31y/M

Mesentery of small bowel

17.5

Yes

SE, CT

Yes

No

DOD(11 m)

 

15

6y/M

Omentum and mesentery

14

Yes

SE

NA

NA

NA

 

16

39y/M

Mesentery of small bowel

15

Yes

SE

NA

NA

NA

 

17

57y/M

Pleura or chest wall

NA

NA

ALKi

NA

NA

NA

Kozu et al. [10]

18

19y/F

Mesentery of small bowel

19

No

SE

Yes(9w)

No

DOD(12w)

Li et al. [11]

19

39y/M

Mesentery of colon

15

No

SE, CT

Yes(4 m)

No

AWD(12 m)

 

20

22y/M

Mesentery of small bowel

6

Yes

SE, CT, ALKi

Yes(3 m, 4 m)

No

AWD(14 m)

Kimbara et al. [12]

21

37/F

Rectum

5

No

SE

No(8 m)

No

NED(8 m)

Current cases

22

55/M

Mesentery of ileum

11

No

SE, CT

Yes(2 m)

No

NED(10 m)

 

23

22/M

Mesentery of colon

20

Yes

SE, ALKi

Yes(2 m)

No

AWD(14 m)

 

24

58/F

Omentum

5.5

No

SE, CT

Yes(2 m)

No

DOD(8 m)

 

25

15/F

Transverse colon

12

No

SE

No(7 m)

No

NED(7 m)

 
  1. ALKi ALK inhibitor, AWD alive with disease, CE cholecystectomy, CT chemotherapy, DOD dead of disease, NA not available, NED no evidence of disease, RT radiation therapy, SE surgical excision