Table 1 Summary of Reported Cases of Pure Form Pancreatic-Type Acinar Cell Carcinomas Arising in the Stomach

1

Sun and Wasserman, 2004.[4]

86/F

antrum

5.0

PDA^p

exophytic polypoid mass with ulcer

0-3/ HPF

trypsin +, chymotrypsin +, A1AT f+, A1ACT f+, CD56 -, Syn -, Cg -, gastrin -

partial gastrectomy

absence

pure gastric form

absence

NM

2

Mizuno et al., 2007.[3]

73/M

pylorus

7.6

GIST or lymphoma^c, IIB^p

submucosal mass invading pancreatic head

NM

A1AT +

pancreatico-duodenectomy

absence

pure form

LN metastasis

liver metastasis at 7 months, alive after 11 months

3

Ambrosini-Spaltro et al., 2009.[1]

52/M

antrum

4.0

PDA^p

ulcerated mass

low mitotic index

A1AT +, Cg -, Syn -, gastrin -

subtotal gastrectomy

presence by pancreatic metaplasia

pancreatic metaplasia

absence

NM

4

Coyne, 2012.[2]

77/F

fundus

4.5

PDA^p

exophytic polypoid mass with ulcer

3/10 HPF

trypsin +, A1AT +, CD56 f+, Syn w+, Cg -, serotonin -, insulin -, glucagon -

partial gastrectomy

absence

pure gastric form

absence

died from complications after 1 month

5

Yonenaga et al., case 2, 2016.[5]

63/M

antrum

6.5

PDA^p

Borrmann type-2

15/10 HPF

chymotrypsin +, A1ACT +, Cg f+, Syn f+, insulin -, glucagon -, gastrin -, somatostatin -

autopsy

absence

pure gastric form

liver

died from coexisting advanced PaDA after 5 months

6

Present case, 2016

54/M

cardia

2.7

GIST or lymphoma^c, IIB^p

exophytic polypoid mass

1/10 HPF

A1AT +, A1ACT +, CD56 w+, DOG1 w+, Syn -, Cg -, TTF-1 -, CD34 -, c-Kit -

laparoscopic wedge resection

absence

pure gastric form

absence

alive without disease after 33 months