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Table 1 Review of reported cases of gastrointestinal ES/PNET

From: Primary Ewing’s sarcoma/primitive neuroectodermal tumor of the ileum: case report of a 16-year-old Chinese female and literature review

Tumor site

Age

Sex

CgA

Syn

CK

CD99

CD117

FLI1

FISH break-apart EWSR1

RT–PCR EWS–FLI1

Metastasis at diagnosis

Treatments

Follow-up

Reference

Esophagus

44

F

-

-

-

+

-

+

+

+

-

Cx

ND

Johnson AD et al.

Esophagus

56

M

-

ND

-

+

ND

ND

ND

+

Lymph nodes

Sx + ImCx

ND

Maesawa C et al.

Esophagus

21

M

ND

ND

-

-

-

ND

+

ND

-

Sx + Rx

ND

Kim SB et al.

Gastric

31

F

ND

ND

-

+

ND

+

-

+

-

Sx + Rx

3 years DFS

Khuri S et al.

Gastric

19

M

ND

ND

ND

+

+

ND

ND

ND

-

Cx

ND

Aras M et al.

Gastric

41

F

+

+

ND

+

+

ND

ND

+

Intra-peritoneal

Sx + Cx + Rx

Died 110 months after surgery

Inoue M et al.

Gastric

30

M

-

-

-

+

ND

ND

ND

ND

-

Sx

6 month DFS

Ankouz A er al

Gastric

14

M

-

-

-

+

+

ND

ND

+

Liver

Sx + Cx

24 months DFS

Czekalla R et al.

Gastric

55

M

+

+

-

+

+

-

ND

+

Lymph nodes

Sx

13 months DFS

Song JM et al.

Gastric

68

M

-

ND

-

+

+

ND

ND

+

Liver

Sx + Cx

Died 13 months after diagnosis

Rafailidis S et al.

Peri-gastric

44

F

-

-

-

+

+

ND

+

ND

-

Sx

20 months DFS

Colovic RB et al.

Gastric

63

F

ND

ND

ND

ND

ND

ND

+

+

-

Sx + Cx

ND

Maxwell AM er al

Colorectal

59

M

ND

+

-

+

-

ND

ND

+

Peritoneal dissemination

Sx

Died 7 months after diagnosis

Kuwabara K et al.

Colorectal

24

F

-

-

-

+

ND

ND

ND

+

-

Sx

20 months DFS

Tokudome N et al.

Colorectal

17

M

-

-

-

+

ND

ND

ND

+

-

Sx + Cx

1 years DFS

Drut R er al

Colorectal

34

F

ND

ND

-

+

ND

ND

ND

+

Liver

Sx + StemCx

7 years DFS

Aboumarzouk OM et al.

Colorectal

53

M

-

ND

-

+

ND

ND

ND

ND

-

Sx + Cx + Rx

Died 2 years after diagnosis

Vardy J et al.

Small bowel

21

F

ND

-

+

+

ND

ND

ND

ND

-

Sx + Cx

10 months DFS

Adair et al.

Small bowel

20

F

ND

ND

ND

+

ND

ND

+

-

-

Sx + Cx

18 months DFS

Kie et al.

Small bowel

13

M

ND

-

+

+

ND

ND

+

ND

-

Sx

1 years DFS

Sarangarajan etal

Small bowel

40

M

ND

+

-

+

ND

ND

+

ND

Intra-peritoneal

Sx + Cx

Died with recurrence 5 months after diagnosis

Horie and Kato

Small bowel

14

M

ND

-

+

+

ND

ND

+

+

-

Sx + Cx

10 month DFS

Graham et al.

Small bowel

9

F

-

-

+

ND

ND

ND

+

+

-

Sx + Cx

Died 25 months after diagnosis

Shek et al.

Small bowel

53

F

ND

ND

ND

+

ND

ND

ND

ND

-

Sx

ND

Balasubram-anina et al.

Small bowel

63

M

ND

ND

ND

+

+

ND

ND

ND

Adrenal glands + lymph nodes

Sx + Cx

ND

Kim et al.

Small bowel

44

M

ND

ND

-

+

ND

ND

ND

ND

Intra-peritoneal

Sx + Cx

Died 13 months after diagnosis

Sethi and Smith

Small bowel

32

M

ND

ND

ND

+

ND

+

+

ND

-

Sx + Cx

6 months DFS

Rodarte Shade et al.

Small bowel

15

F

ND

ND

ND

ND

ND

ND

+

+

-

Sx + Cx

ND

Vignail et al.

Small bowel

18

M

ND

ND

ND

ND

ND

ND

ND

ND

-

Sx + Cx

ND

Boehm et al.

Small bowel

18

M

+

+

+

+

+

+

+

+

Liver

Sx

Died 8 months after diagnosis

Milione M et al.

Small bowel

20

M

+

+

+

+

+

+

+

+

Liver

Sx + Cx

Died 28 months after diagnosis

Milione M et al.

Small bowel

42

M

+

+

+

+

+

+

+

+

-

Sx + Cx

Died 11 months after diagnosis

Milione M et al.

Small bowel

45

M

+

+

+

+

+

+

+

+

-

Sx + Cx

Died 13 months after diagnosis

Milione M et al.

Small bowel

15

F

+

+

+

+

+

+

+

+

-

Sx + Cx + Rx

28 months DFS

Milione M et al.

Small bowel

57

M

+

+

+

+

+

+

+

+

-

Lost

Lost

Milione M et al.

Small bowel

28

F

+

+

+

+

-

-

+

+

Liver

Sx + Cx

204 months DFS

Milione M et al.

  1. F Female, M Male, ND Not done, Sx Surgery, Cx Chemotherapy, ImCx Immuno chemotherapy, StemCx Stem cell based chemotherapy, Rx Radiotherapy, DFS Disease free survival