From: Nuclear TFE3 expression is a diagnostic marker for Desmoid-type fibromatosis
DTF (n = 46) | NF (n = 14) | Neurofibroma (n = 5) | Leiomyoma (n = 3) | GIST (n = 10) | DFSP (n = 5) | IMT (n = 2) | SS (n = 5) | SEF (n = 2) | Scar (n = 4) | |
---|---|---|---|---|---|---|---|---|---|---|
Age(y) | 15–65 | 22–65 | 55–73 | 49–68 | 36–72 | 19–47 | 27–29 | 47–72 | 34–49 | 10–56 |
Mean(y) | 36 | 40 | 65.2 | 57.3 | 55.4 | 34.4 | 28 | 55.7 | 41.5 | 28.8 |
male | 18 | 6 | 3 | 1 | 7 | 1 | 2 | 3 | 1 | 1 |
female | 28 | 9 | 2 | 2 | 3 | 4 | 0 | 2 | 1 | 3 |
Location | ||||||||||
Abdominal wall | 16 | 0 | 1 | 1 | 0 | 1 | 0 | 0 | 0 | |
Abdominal cavity | 15 | 0 | 1 | 1 | 10 | 0 | 1 | 2 | 0 | |
back | 3 | 2 | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |
Chest | 2 | 1 | 1 | 1 | 0 | 2 | 0 | 0 | 0 | 2 |
Hipshot | 2 | 0 | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
Limb | 7 | 10 | 1 | 0 | 0 | 1 | 0 | 5 | 0 | 2 |
Breast | 1 | 1 | 0 | 0 | 0 | 1 | 0 | 0 | 0 | 0 |