Characteristics | n (%); median (IQR) |
---|---|
Sex | |
▪ Male | 27 (54) |
▪ Female | 23 (46) |
Age at Kasai procedure performed (days) | 102.5 (75.75–142.25) |
Type of biliary atresia (BA) | |
▪ 1 | 2 (4) |
▪ 2A | 18 (36) |
▪ 2B | 6 (12) |
▪ 3 | 24 (48) |
Pre-operative laboratory findings (normal range) | |
▪ Total bilirubin (≤1.0 mg/dL) | 10.76 (7.86–13.6) |
▪ Direct bilirubin (0–0.2 mg/dL) | 8.17 (6.45–11.59) |
▪ Aspartate aminotransferase (≤40 U/L) | 187 (120.5–242.25) |
▪ Alanine aminotransferase (≤41 U/L) | 119 (68.75–168.75) |
▪ Gamma glutamyl transferase (7–64 U/L) | 566 (268.5–946.75) |
▪ Alkaline phosphatase (≤462 U/L) | 471 (361–648) |
▪ Albumin (3.9–4.9 g/dL) | 3.55 (3.23–4.14) |
▪ International normalized ratio (0.9–1.1) | 1.025 (0.94–1.205) |
▪ Platelet (150–450 × 103/uL) | 270 (218.75–409.25) |
Outcomes | |
▪ Survived | 26 (52) |
▪ Died | 24 (48) |
Causes of death | |
▪ Septic shock | 14 (56.5) |
▪ Hemorrhagic shock | 4 (17.4) |
▪ Multiple organ dysfunction syndrome | 2 (8.7) |
▪ Acute respiratory distress syndrome | 4 (17.4) |