|
Sex
|
|
▪ Male
|
27 (54)
|
|
▪ Female
|
23 (46)
|
|
Age at Kasai procedure performed (days)
|
102.5 (75.75–142.25)
|
|
Type of biliary atresia (BA)
|
|
▪ 1
|
2 (4)
|
|
▪ 2A
|
18 (36)
|
|
▪ 2B
|
6 (12)
|
|
▪ 3
|
24 (48)
|
|
Pre-operative laboratory findings (normal range)
|
|
▪ Total bilirubin (≤1.0 mg/dL)
|
10.76 (7.86–13.6)
|
|
▪ Direct bilirubin (0–0.2 mg/dL)
|
8.17 (6.45–11.59)
|
|
▪ Aspartate aminotransferase (≤40 U/L)
|
187 (120.5–242.25)
|
|
▪ Alanine aminotransferase (≤41 U/L)
|
119 (68.75–168.75)
|
|
▪ Gamma glutamyl transferase (7–64 U/L)
|
566 (268.5–946.75)
|
|
▪ Alkaline phosphatase (≤462 U/L)
|
471 (361–648)
|
|
▪ Albumin (3.9–4.9 g/dL)
|
3.55 (3.23–4.14)
|
|
▪ International normalized ratio (0.9–1.1)
|
1.025 (0.94–1.205)
|
|
▪ Platelet (150–450 × 103/uL)
|
270 (218.75–409.25)
|
|
Outcomes
|
|
▪ Survived
|
26 (52)
|
|
▪ Died
|
24 (48)
|
|
Causes of death
|
|
▪ Septic shock
|
14 (56.5)
|
|
▪ Hemorrhagic shock
|
4 (17.4)
|
|
▪ Multiple organ dysfunction syndrome
|
2 (8.7)
|
|
▪ Acute respiratory distress syndrome
|
4 (17.4)
|