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Table 1 Summary of clinicopathological features of FA-DLBCL reported cases and our case

From: Fibrin-associated diffuse large B-cell lymphoma with plasmacytic differentiation: case report and literature review

Author

Cases

Age

Sex

Location

Diagnosis

Phenotype

EBV latency

Stage

Adjuvant treatment

Follow-up (months)

Garces et al, 2019 [7]

1

50

M

Left atrial myxoma

FA-DLBCL

Non-GC

NA

Localized

None

65-WER

Zanelli et al, 2019 [8]

1

75

F

Adrenal pseudocyst

FA-DLBCL

Non-GC

NA

NA

NA

NA

Boyer et al, 2017 [4]

12

54

F

Left atrial myxoma

FA-DLBCL

NA

NA

NA

NA

130-WER

55

F

Left atrial myxoma

FA-DLBCL

Non-GC

Type III

NA

None

Died 2 mo-WER

54

M

Left atrial myxoma

FA-DLBCL

Non-GC

Type III

Localized

None

Died 26 mo-recurrent atrial mass

56

M

Aortic aneurysm

FA-DLBCL

Non-GC

Type III

Localized

R-CHOP × 6

24-persistent local disease

68

M

Arterial thromboembolism

FA-DLBCL

Non-GC

Type III

NA

R-COEP × 2

Died 10 mo-WER

71

M

Aortobifemoral prosthesis

FA-DLBCL

Non-GC

Type II-III

NA

None

10-WER

79

M

Testicular hematoma

FA-DLBCL

Non-GC

Type III

NA

None

Died 17 mo-WER

25

M

Subdural hematoma

FA-DLBCL

Non-GC

Type II-III

Localized

None

7-WER

37

F

Splenic pseudocyst

FA-DLBCL

Non-GC

NA

Localized

R-CHOP × 3

32-WER

73

M

Retroperitoneal pseudocyst

FA-DLBCL

Non-GC

NA

Localized

R-CHOP × 6

43-WER

70

M

Adrenal pseudocyst

FA-DLBCL

Non-GC

Type III

Localized

None

14-WER

44

M

Retroperitoneal pseudocyst

FA-DLBCL

Non-GC

Type III

Localized

CHOP × 5

84-WER

Kirschenbaum et al, 2017 [5]

1

81

M

Arachnoid cyst

FA-DLBCL

NA

NA

Localized

R-L x NA

NA

Yan et al, 2017

4

46

F

Left atrial myxoma

DLBCL-CI

Non-GC

Type III

Localized

None

10-WER

61

F

Left atrial myxoma

DLBCL-CI

GC

Type III

Localized

None

7-WER

54

M

Left atrial myxoma

DLBCL-CI

Non-GC

Type III

Localized

None

7-WER

46

F

Left atrial myxoma

DLBCL-CI

Non-GC

Type III

Localized

None

3-WER

Aguilar et al, 2015 [1]

1

52

M

Left atrial myxoma

FA-DLBCL

Non-GC

Type III

Localized

None

42-WER

Tapan et al, 2015 [6]

1

49

M

Left atrial myxoma

EBV-DLBCL

Non-GC

Type III

Localized

R-CHOP × 6

12-WER

Gruver et a., 2012 [2]

3

55

M

Aortic root graft

FA-DLBCL

Non-GC

Type III

Localized

R-CEOP × 8

16-WER

56

M

Left atrium

FA-DLBCL

Non-GC

Type III

Localized

R-CHOP × 6

8-WER

75

M

Mitral valve

FA-DLBCL

Non-GC

EBV -

Localized

R-CVP × 1 and R-CHOP × 6

39-WER

Svec et al, 2012 [4]

1

60

F

Left atrial myxoma

EBV-DLBCL

Non-GC

Type III

Localized

R-CHOP × 6

7-WER

Loong et al, 2010 [3]

4

29

M

Splenic cyst

DLBCL-CI

Non-GC

Type III

Localized

Rituximab × 6

6-WER

88

M

Right hydrocele

DLBCL-CI

Non-GC

Type III

NA

Lost to follow-up

NA

70

F

Left atrial myxoma

DLBCL-CI

Non-GC

Type III

Localized

R-CEOP × 4

Died 5 mo-WER

78

M

Knee prosthesis

DLBCL-CI

Non-GC

Type III

Localized

RT × 7

84 (7 y)-WER

Present case

1

57

F

Left atrial myxoma

Plasmacytic FA-DLBCL

Non-GC

Type I

NA

None

1-Loss of follow-up

  1. FA-DLBCL fibrin-associated diffuse large B-cell lymphoma, DLBCL-CI DLBCL associated with chronic inflammation, Non-GC non-germinal center, GC germinal center, NA not available, WER without evidence of recurrence, R-L rituximab, lenalidomide, R-CHOP rituximab, cyclophosphamide, doxorubicin, vincristine and prednisone, R-CVP rituximab, cyclophosphamide, vincristine and prednisone, R-COEP rituximab, cyclophosphamide, vincristine, etoposide, prednisone, R-CEOP rituximab, cyclophosphamide, etoposide, oncovin, and prednisone, RT radiotherapy