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Table 1 Clinicopathological and prognostic characteristics of epithelioid and spindle rhabdomyosarcoma

From: Epithelioid and spindle rhabdomyosarcoma with TFCP2 rearrangement in abdominal wall: a distinctive entity with poor prognosis

Study

Age (Y)/Sex

Size (cm)

Location

Rec/Met

Treatment

Follow-up (Mon)

Outcome

Dashti/2018

70–75/M

4

Mandible

No

No

2

AWND

Wong/2019

20–25/M

8

Nasal cavity

No

Exc, CR

4

DD

Agaram/2019

25–30/F

NA

Skull

NA

NA

NA

NA

Agaram/2019

30–35/F

NA

Maxilla

NA

NA

NA

NA

Agaram/2019

20–25/M

NA

Femur

No

Exc

108

AWND

Agaram/2019

35–40/F

NA

Iliac

NA

NA

NA

NA

Agaram/2019

20–25/F

NA

Femur

L

NA

30

AWD

Tagami/2019

70–75/F

Biopsy

Ver

No

CR

6

AWD

Zhu/2019

70–75/F

4

Maxillary gingiva

NA

NA

NA

NA

Le Loarer/2019

15–20/F

9

Sphenoid

No

Exc, CR

15

DD

Le Loarer/2019

25–30/F

10

Sacrum

L, Med, LN

Ch

4

DD

Le Loarer/2019

35–40/F

NA

Peritoneum

No

Ch

2

DD

Le Loarer/2019

30–35/M

NA

Hard palate & upper lip

Ver & ribs & pelvis

Ch

8

DD

Le Loarer/2019

20–25/M

15

Orbito & temporal & sphenoid

LP

CR

6

DD

Le Loarer/2019

85–90/M

6.5

Inguinal

LP

Exc

6

DD

Le Loarer/2019

15–20/F

5.1

Femur

LP

Exc, Ch

8

DD

Le Loarer/2019

15–20/F

5.3

Cervico-occipital

LP

Exc, Ch

15

AWD

Le Loarer/2019

30–35/M

11.8

Left occipital

L, Med

Exc, Ch

6

DD

Le Loarer/2019

30–35/M

4.5

Mandible

L

Exc, Ch

14

AWD

Le Loarer/2019

55–60/F

1.6

Mandible

No

Exc, CR

21

AWND

Le Loarer/2019

10–15/F

5.5

Mandible

No

Exc, CR

21

AWND

Le Loarer/2019

10–15/F

NA

Maxilla

NA

NA

NA

DD

Le Loarer/2019

25–30/M

3.4

Mandible

No

Exc, Ch

20

AWND

Chrisinger/2020

20–30/F

5

Frontal bone

L

Exc, CR

17

DD

Chrisinger/2020

20–25/F

13.6

Pelvic bones

L, Ver

CR

11

DD

Xu/2021

20–25/M

NA

Mandible

LN

NA

NA

NA

Xu/2021

30–35/M

NA

Mandible

No

NA

10

AWD

Xu/2021

15–20/M

NA

Mandible

L, Bone, LN

Exc, CR

20

DD

Xu/2021

40–45/F

NA

Mandible

NA

NA

NA

NA

Xu/2021

15–20/M

NA

Skull

NA

NA

NA

NA

Xu/2021

25–30/M

NA

Skull

L

NA

2

AWD

Xu/2021

40–45/F

NA

Neck

NA

NA

NA

NA

Our case

30–35/F

5

Abdominal wall

Med

Exc, TCM

24

AWD

  1. Rec/Met: Reccurence/Metastasis; L: lung; Med: mediastinal; LN: lymph node; LP: local progression; Ver: Vertebra; Y: years; Exc: Excision; Ch: Chemotherapy; CR: Chemoradiotherapy; TCM: Traditional Chinese Medicine; NA: not available; Mon: months; AWND: alive with no disease; AWD: alive with disease; DD: died of disease