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Table 2 Clinicopathological and prognostic characteristics of epithelioid rhabdomyosarcoma

From: Epithelioid and spindle rhabdomyosarcoma with TFCP2 rearrangement in abdominal wall: a distinctive entity with poor prognosis

Study

Age (Y)/Sex

Size (cm)

Location

Rec/Met

Treatment

Follow-up (Mon)

Outcome

Suarez-Vilela/2004

70–75/M

5.5

Retroauricular & SM

LN

Exc, Ch

3

DD

Fujiwaki/2008

50–55/F

6.5

Fallopian tube

LN

Exc, Ch

6

DD

Bowe/2011

70–75/M

5

Parotid gland LN

No

Exc, Ch

12

AWND

Jo/2011

70–75/M

NA

Knee

L, LN

Exc, CR

10

DD

Jo/2011

70–75/M

5.3

Neck

LN

Exc, Ch

5

DD

Jo/2011

75–80/F

NA

Neck

Med, LN

Rad

2

DD

Jo/2011

30–35/M

8

Arm

L, bone

Exc, CR

60

DD

Jo/2011

20–25/M

8.5

Thigh

L, Liver

Exc, Ch

6

DD

Jo/2011

10–15/F

NA

Elbow

No

Exc, CR

47

AWND

Jo/2011

35–40/M

8

Forearm

L, LN

Exc, CR

10

DD

Jo/2011

75–80/M

8

Shoulder

L

Exc

24

DD

Jo/2011

70–75/M

5

Chesk wall

No

Exc, Ch

36

AWND

Zin/2014

5–10/M

NA

Para-meningeal

LN

Exc, Ch

96

AWND

Zin/2014

5–10/M

3.3

Para-meningeal

NA

Exc, Ch

120

AWND

Zin/2014

10–15/F

4

Arm

No

Exc, Ch

72

AWND

Zin/2014

5–10/F

8.3

Arm

LN

Exc, Ch

24

AWND

Zin/2014

5–10/M

4

Orbit

No

Exc, Ch

48

AWND

Yu/2015

15–20/F

15

Left thigh

NA

NA

4

DD

Yu/2015

75–80/M

12

Left waist & back

Rec

Exc, Rad

13

AWND

Yu/2015

60–65/M

12.5

Left chesk wall

LN

Exc

2

AWND

Yu/2015

55–60/M

2.5

Left femur

L

Exc, Ch

14

DD

Yu/2015

80–85/F

NA

Left upper eyelid

Preaurical

Exc

7

DD

Yu/2015

35–40/M

3.5

Thyroid gland

No

Exc, CR

6

AWND

Jokoji/2015

65–70/F

 

Neck & abdomen

LN

Ch

6

DD

Renshaw/2019

50–55/F

NA

Pleural & L & RP

NA

NA

21(Days)

DD

Valerio/2020

80–85/M

3

Neck cutaneous

NA

NA

0

DD

De Aguiar/2020

15–20/M

6

Jaw

NA

Exc, Ch

5

DD

Rodgers/2021

70–75/M

11.5

Pelvic

LN

No

5(Days)

DD

  1. Rec/Met: Reccurence/Metastasis; L: lung; Med: mediastinal; LN: lymph node; LP: local progression; Ver: Vertebra; SM: submandibular; Y: years; Exc: Excision; Ch: Chemotherapy; CR: Chemoradiotherapy; Rad: Radiotherapy; TCM: Traditional Chinese Medicine; NA: not available; Mon: months; AWND: alive with no disease; AWD: alive with disease; DD: died of disease