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Table 3 Clinicopathological and prognostic characteristics of spindle cell/sclerosing rhabdomyosarcoma

From: Epithelioid and spindle rhabdomyosarcoma with TFCP2 rearrangement in abdominal wall: a distinctive entity with poor prognosis

Study

Age (Y)/Sex

Size (cm)

Location

Rec/Met

Treatment

Follow-up (Mon)

Outcome

Mentzel/2006

35–40/M

13

Forearm

L

Exc

24

DD

Mentzel/2006

55–60/M

19

Hip

No

Exc

46

AWND

Mentzel/2006

60–65/M

11

Lower leg

L

Exc

12

DD

Mentzel/2006

75–80/F

4

Thigh

No

Exc

15

AWND

Mentzel/2006

50–55/M

8

Neck

No

Exc, Ch

48

AWND

Gavino/2010

30–35/F

NA

Right leg

Met

Exc

16

AWD

Rekhi/2014

15–20/M

NA

Oral cavity and maxilla

No

Exc, CR

12

AWD

Rekhi/2014

15–20/M

NA

Paratesticular

LN

Exc

12

AWND

Rekhi/2014

60–65/M

NA

Thigh

L

Exc, Ch

5

AWD

Rekhi/2014

30–35/F

NA

Cheeck

NA

CR

16

DD

Rekhi/2014

35–40/M

NA

Paraspinal

Lung

Exc

2

AWD

Mikubo/2014

25–30/F

13

Chest wall

Rec

Exc, Ch

18

AWD

Yasui/2015

20–25/F

> 5

Pharynx

LN

Exc, CR

27.1

DD

Yasui/2015

25–30/F

> 5

Malar region

Rec & Met

Exc, Rad

74.6

DD

Yasui/2015

35–40/M

> 5

Dorsum of the foot

No

Exc

144.7

AWND

Yasui/2015

15–20/M

> 5

Temporal region

Rec & Met

Exc, CR

24.3

DD

Yasui/2015

45–50/M

< 5

Scrotum

Rec & Met

Exc, Ch

14.2

DD

Yasui/2015

10–15/M

> 5

Scrotum

No

Exc, Ch

201

AWND

Yasui/2015

20–25/F

> 5

Malar region

No

Exc, CR

39.9

AWND

Yasui/2015

25–30/F

> 5

Intrathoracic space, thoracic wall

Rec

Exc, CR

40.6

DD

Yasui/2015

15–20/F

< 5

Malar region, pharynx

Rec & Met

CR

116.8

DD

Yasui/2015

15–20/M

> 5

Parapharyngeal space

Rec & Met

Exc, CR

24.7

DD

Yasui/2015

20–25/F

< 5

Tongue

Rec & Met

Exc, Ch

38.4

DD

Yasui/2015

35–40/M

> 5

Prostate

NA

Exc, Ch

89

AWND

Yasui/2015

25–30/M

> 5

Malar region

NA

Exc, CR

14.6

AWND

Yasui/2015

5–10/M

> 5

Parapharyngeal space

Rec

Exc, CR

14.4

AWND

Yasui/2015

20–25/M

> 5

Scrotum

NA

Exc, Ch

4.7

AWD

Zhao/2015

40–45/M

5.2

Left upper arm

NA

Exc, CR

24

DD

Zhao/2015

30–35/M

14

Abdomen wall

Rec

Exc

10

AWD

Zhao/2015

45–50/M

2.4

Larynx

No

Exc, Rad

5

AWND

Zhao/2015

0–5/F

2.8

Left orbit

NA

Exc

5

AWD

Zhao/2015

25–30/M

5

Nasopharynx

NA

Exc

1

AWD

Zhao/2015

50–55/M

21

Left thigh

Rec & Met

Exc

12

AWD

Zhao/2015

25–30/F

3.4

Back of right hand

No

Exc

1

AWND

Zhao/2015

15–20/M

16.5

Right groin

No

Exc, Ch

6

AWND

Zhao/2015

35–40/F

4.8

Left pars buccalis

No

Exc

8

AWND

Zhao/2015

55–60/F

2.3

Right parotid gland

No

Exc

13

AWND

Alaggio/2016

0–5/F

NA

Back

NA

NA

108

AWND

Alaggio/2016

0–5/F

NA

Back

NA

NA

72

AWND

Alaggio/2016

0–5/F

NA

Lower neck/back

NA

NA

96

AWND

Alaggio/2016

15–20/M

NA

Paravertebral

NA

NA

24

DD

Alaggio/2016

10–15/F

NA

Buttock

NA

NA

6

DD

Alaggio/2016

5–10/M

NA

Thigh

NA

NA

1

AWND

Alaggio/2016

5–10/M

NA

Head and Neck

Rec

NA

36

AWD

Alaggio/2016

5–10/F

NA

Head and Neck

NA

NA

24

DD

Alaggio/2016

0–5/M

NA

Intra-abdomina

NA

NA

156

AWND

Alaggio/2016

15–20/M

 

Paratesticular

  

24

AWND

Alaggio/2016

0–5/F

NA

Ovary/salpinx

NA

NA

48

DD

Alaggio/2016

10–15/M

NA

Paratesticular

NA

NA

24

AWND

Walther/2016

0–5/F

5

Thigh

NA

Exc, Ch

16

DD

Owosho/2016

15–20/F

3.5

Buccal/masticator space

NA

Exc, CR

31

AWND

Owosho/2016

25–30/M

10.5

Buccal/masticator space

NA

CR

12

DD

Owosho/2016

30–35/M

5.8

Soft tissue mandible

Rec & Met

Exc, CR

65

DD

Owosho/2016

70–75/M

9.1

Neck

NA

Exc, CR

29

AWND

Owosho/2016

40–45/M

4.5

Soft tissue mandible

NA

Exc, Rad

4

AWND

Owosho/2016

60–65/M

8.3

Hypopharynx

NA

Exc, CR

14

DD

Owosho/2016

30–35/M

0.8

Tongue

NA

Exc, Ch

94

AWND

Owosho/2016

0–5/F

1

Nasolabial/cheek

NA

Exc, Rad

7

AWND

Smith/2017

20–25/M

5.1

Oral cavity

No

Exc, CR

48

AWND

Momosaka/2017

65–70/F

NA

Intracranial

Rec

Exc

3

DD

Agaram/2019

10–15/F

NA

Head and Neck

Rec & Met

CR

48

AWND

Agaram/2019

35–40/M

NA

Lower leg

NA

CR

60

AWND

Agaram/2019

75–80/M

NA

Lower leg

Rec & Met

CR

32

DD

Whittle/2019

0–5/M

2.7

Palpable

No

Exc, Ch

15

AWND

Whittle/2019

0–5/F

5.2

Chest wall

No

Exc, Ch

12

AWND

Whittle/2019

0–5/F

NA

Chest wall

No

Exc, Ch

13

AWND

Whittle/2019

0–5/F

4.2

Left foot

No

Exc, Ch

7

AWND

Akki/2019

55–60/F

18.5

Liver

No

Ch

12

AWND

Cordier/2021

0–5/M

4.8

Below the left scapula

No

Ch

6

AWD

Jariod-Ferrer/2021

25–30/M

0.9

Tongue

Rec

Exc, CR

48

AWD

Wang/2021

55–60/M

7

Left temporal scalp

No

Exc, CR

3

AWND

  1. Rec/Met: Reccurence/Metastasis; L: lung; Med: mediastinal; LN: lymph node; LP: local progression; Ver: Vertebra; Y: years; Exc: Excision; Ch: Chemotherapy; CR: Chemoradiotherapy; Rad: Radiotherapy; TCM: Traditional Chinese Medicine; NA: not available; Mon: months; AWND: alive with no disease; AWD: alive with disease; DD: died of disease