Table 1 Clinical and demographic characteristics of patients with UESL. GTR: Gross tumor resection
Patient | Age | Sex | Tumor Location | Extrahepatic Metastasis | Symptoms | COG Stage | Laboratory Findings | CT Imaging Findings | Surgery | Radiation Therapy | Chemotherapy | Recurrence | Outcome (years from diagnosis |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Case 1 | 2y 8 M | M | Right lobe | – | Abdominal pain, Fever | I | ↑ AST, ALT | Lobulated hypodense mass with peripheral irregularity and focal calcification | GTR | – | + (Vincristine, Actinomycin, Cyclophosphamide, Doxorubicin, Ifosfamide, Etoposide) | – | No evidence of disease (8y) |
Case 2 | 14y | F | Right lobe | – | Abdominal pain, anorexia, weight loss | I | ↑Plt, ↓Hb | Heterogeneous lesion with intratumoral hemorrhage and multiple foci of necrosis | GTR | – | + | – | No evidence of disease (6y) |
Case 3 | 13y | F | Right lobe | – | Abdominal pain, nausea/vomiting | I | ↑CA-125 | Hypodense lesion with faint peripheral and internal septation | GTR | – | – | – | No evidence of disease (6y) |
Case 4 | 12y | F | Right lobe | – | Abdominal pain | III | ↓Hb | Cystic mass with solid nodules and septation | GTR | + | + | + | Died of disease (3y) |
Case 5 | 3y 6 M | M | Right lobe | – | Abdominal pain | I | ↑INR, ↓ Hb | Complicated hypoattenuated mass containing septation | GTR | – | + (Actinomycin, Cyclophosphamide, Vincristine) | – | No evidence of disease (3.5y) |
Case 6 | 12 y | F | Right lobe | – | Abdominal pain, nausea/vomiting | I | ↑ AST, ALT | Hypoattenuating lesion with multiple thick septa | GTR | + | + | + | Under treatment (3y) |
Case 7 | 5 y | M | Right lobe | – | Abdominal pain, nausea/vomiting | I | ↑ AST, ALT | Cystic mass with internal septation | GTR | – | + (Vincristine, Doxorubicin, Cyclophosphamide) | – | No evidence of disease (2y) |
Case 8 | 16 y | F | Right lobe | – | Abdominal pain, chills, fever | II | ↑INR, ↑ ESR, ↓ Hb | Heterogenous hypodense mass | GTR | – | + | – | No evidence of disease (1y) |